Bronchial Atresia
نویسنده
چکیده
Bronchial atresia is an interesting congenital abnormality because of its variable appearance and its semblance to certain acquired diseases. It is characterized by a branching mass formed by mucus that dilates the proximal bronchi to the atretic segment. The distal lung to atresia can develop normally but it shows a paucity of blood vessels and is hyperinflated due to unidirectional collateral air drift through intraalveolar pores of Kohn, bronchoalveolar channels of Lambert and interbronchiolar pores of Martin from the adjacent normal lung. These collateral communications act as a check-valve mechanism allowing the air to enter but not to leave the distal lung.
منابع مشابه
Unique Approach to Diagnosing and Treating Congenital Bronchial Atresia (CBA): A Case Series
Congenital bronchial atresia (CBA) is a rare airway anomaly resulting in termination of a bronchus into a blind pouch with associated mucoid impaction and segmental hyperinflation. The etiology of CBA is related to vascular insufficiency to the bronchial bud during embryologic development. Controversy exists regarding the best approach to treatment for CBA and relating symptoms to the presence ...
متن کاملUnilateral hyperlucent lung associated with bronchial atresia mimicking Swyer-James syndrome.
Bronchial atresia is a rare pulmonary anomaly characterized by a blindly-terminating bronchus, mucoid impaction, and hyperinflation of the obstructed segment of the lung.1 Chest radiographic findings typically show mucoid impaction, segmental overinflation, and hypovascularity, although most patients do not have any respiratory symptoms.1,2 We herein present 2 cases of bronchial atresia with un...
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Two cases of congenital bronchial atresia with pectus excavatum are reported. Costosternal retraction during the efforts to overcome the airway obstruction due to encroachment on normal lung tissue by the hyperinflated segments may play a part in causing pectus excavatum.
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Bronchial atresia is a rare pulmonary developmental anomaly characterized by the presence of a focal obliteration of a segmental or lobar bronchial lumen. The lung distal to the atretic bronchus is typically emphysematous along with the presence of mucus filled ectatic bronchi (mucoceles). BA is usually asymptomatic but pulmonary infections can rarely develop in the emphysematous lung distal to...
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